Papillon-Lefevre Syndrome: Challenge for Periodontal Management

Authors

  • Krishna Prasad Lamichhane Periodontology and Oral Implantology Unit, Department of Dental Surgery, National Academy of Medical Sciences, Bir Hospital, Kathmandu, Nepal
  • Shaili Pradhan Periodontology and Oral Implantology Unit, Department of Dental Surgery, National Academy of Medical Sciences, Bir Hospital, Kathmandu, Nepal
  • Ranjita Shreshta Gorkhali Periodontology and Oral Implantology Unit, Department of Dental Surgery, National Academy of Medical Sciences, Bir Hospital, Kathmandu, Nepal
  • Pramod Kumar Koirala Periodontology and Oral Implantology Unit, Department of Dental Surgery, National Academy of Medical Sciences, Bir Hospital, Kathmandu, Nepal

DOI:

https://doi.org/10.3126/jnspoi.v3i2.30891

Keywords:

Diagnosis, genetic mutation, management, manifestations, palmoplantar keratosis

Abstract

Papillon-Lefèvre syndrome (PLS) is a rare autosomal recessive disorder associated with rapidly progressing periodontitis leading to premature loss of deciduous and permanent dentition and diffuse palmoplantar keratosis. Immunologic alterations, genetic mutations, and role of bacteria are some aetiologic factors. Patients present with early periodontal destruction, so periodontists play a significant role in diagnosis and management. This paper reports a case of Papillon- Lefevre syndrome with its clinical manifestations and challenges for periodontal management which was diagnosed in dental department.

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Published

2019-12-31

How to Cite

Lamichhane, K. P., Pradhan, S., Gorkhali, R. S., & Koirala, P. K. (2019). Papillon-Lefevre Syndrome: Challenge for Periodontal Management. Journal of Nepalese Society of Periodontology and Oral Implantology, 3(2), 84–86. https://doi.org/10.3126/jnspoi.v3i2.30891

Issue

Vol. 3 No. 2 (2019)

Section

Case Reports

License

© Nepalese Society of Periodontology and Oral implantology (NSPOI)

Licenced by Creative Commons Attribution 4.0 International License.