Chiari Malformation-I with Syringomyelia: A Non-specific Presentation and Surgical Consideration

Authors

  • Jemesh S Maharjan Department of Neurosurgery Annapurna Neurological Institute and Allied Sciences Maitighar, Kathmandu
  • Pranaya Shrestha Department of Neurosurgery Annapurna Neurological Institute and Allied Sciences Maitighar, Kathmandu
  • Avinash Chandra Department of Neurosurgery Annapurna Neurological Institute and Allied Sciences Maitighar, Kathmandu
  • Pravesh Rajbhandari Department of Neurosurgery Annapurna Neurological Institute and Allied Sciences Maitighar, Kathmandu
  • Samir Acharya Department of Neurosurgery Annapurna Neurological Institute and Allied Sciences Maitighar, Kathmandu
  • Resha Shrestha Department of Neurosurgery Annapurna Neurological Institute and Allied Sciences Maitighar, Kathmandu
  • Robin Bhattarai Department of Neurosurgery Annapurna Neurological Institute and Allied Sciences Maitighar, Kathmandu
  • Basant Pant Department of Neurosurgery Annapurna Neurological Institute and Allied Sciences Maitighar, Kathmandu

DOI:

https://doi.org/10.3126/njn.v13i2.20489

Keywords:

Chiari malformation-I, Posterior fossa decompression, Syringomyelia, Tonsillar herniation, Syringo-subarachnoid shunt

Abstract

Chiari Malformation-I is a congenital disorder characterized by the anatomical defect of the base of skull with tonsillar herniation (≥5 mm) below the foramen magnum, which is detected on MRI. It has a diverse range of symptoms with non-specific presentation leading to the chances of misdiagnosis and untimely recognition of the disorder. Syringomyelia is the most common result of Chiari-I. The selection of surgical or non-surgical management depends upon the patient symptoms and the presence of absence of Syringomyelia. The objective of this case report is to give a broad perspective on Chiari Malformation-I from the symptoms and clinical findings obtained in a patient with Syringomyelia associated with Chiari Malformation-I and to discuss about the different surgical options as well as the psychological support required for the management of the condition.

Nepal Journal of Neuroscience. Vol. 13, No. 2, 2016, Page: 105-108

 

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Published

2016-12-01

How to Cite

1.
Maharjan JS, Shrestha P, Chandra A, Rajbhandari P, Acharya S, Shrestha R, Bhattarai R, Pant B. Chiari Malformation-I with Syringomyelia: A Non-specific Presentation and Surgical Consideration. Nep J Neurosci [Internet]. 2016 Dec. 1 [cited 2024 Nov. 12];13(2):105-8. Available from: https://nepjol.info/index.php/NJN/article/view/20489

Issue

Vol. 13 No. 2 (2016)

Section

Case Report