Multiple odontogenic keratocysts associated with Gorlin-Goltz syndrome

Authors

  • S Dixit Lecturer, Dental Department, Kathmandu Medical College, Sinamangal, Nepal
  • S Acharya Lecturer, Dental Department, KIST Medical College, Lalitpur, Nepal.
  • PB Dixit Lecturer, Dental Department, Kathmandu Medical College, Sinamangal, Nepal

DOI:

https://doi.org/10.3126/kumj.v7i4.2765

Keywords:

Nevoid basal cell carcinoma syndrome, Gorlin-Goltz syndrome, Odentogenic keratocyst, Calcification of falx cerebri

Abstract

Gorlin-Goltz syndrome or Nevoid basal cell carcinoma syndrome is an autosomal dominant disorder with a predisposition to cancer. Features like basal cell carcinoma, odontogenic keratocysts, calcification of falx cerebri, bifid ribs, pits on palms and soles and hypertelorism are evident. A case of this rare disease seen on a 13 year old female patient is presented here, where multiple odontogenic keratocysts were causing disfigurement of the lower jaw as well as displacement and malocclusion of the lower teeth.

Key words: Nevoid basal cell carcinoma syndrome; Gorlin-Goltz syndrome; Odentogenic keratocyst; Calcification of falx cerebri.

DOI: 10.3126/kumj.v7i4.2765

Kathmandu University Medical Journal (2009) Vol.7, No.4 Issue 28, 414-418

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How to Cite

Dixit, S., Acharya, S., & Dixit, P. (2010). Multiple odontogenic keratocysts associated with Gorlin-Goltz syndrome. Kathmandu University Medical Journal, 7(4), 414–418. https://doi.org/10.3126/kumj.v7i4.2765

Issue

Vol. 7 No. 4 (2009)

Section

Case Notes