Prune belly syndrome - A case report

Authors

  • D Rupshikha Dept. of Anatomy, Prathima Institute of Medical Sciences
  • MJ Phukon Dept. of Anatomy, Prathima Institute of Medical Sciences
  • GR Kusre Dept of Anatomy, Assam Medical College
  • N Satyanarayana College of Medical Sciences, Bharatpur
  • P Sunitha College of Medical Sciences, Bharatpur

DOI:

https://doi.org/10.3126/jcmsn.v7i3.6709

Keywords:

Abdominal muscle deficiency, urogenital defects, persistant cloaca, renal dysplasia, coarctation of aorta

Abstract

Prune Belly Syndrome (PBS) is a rare congenital anomaly. A male baby was received from the Department of Paediatrics, Assam Medical College hospital which died on the second day of birth. It was a diagnosed case of Prune Belly Syndrome (PBS) due to its flabby abdominal wall ballooning out in flanks and skin creases radiating laterally and downwards from the umbilicus - "Prune" like appearance. It was observed that the baby had congenital absence of abdominal muscles and undescended testis. On dissection, associated defects of urinary tract and gastro intestinal tract, persistent cloaca and preductalcoarctation of aorta were noted. The aetiology of this case owes for an overall mesenchymal defect.

DOI: http://dx.doi.org/10.3126/jcmsn.v7i3.6709

Journal of College of Medical Sciences-Nepal, 2011, Vol-7, No-3, 48-52

 

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Published

2012-08-28

How to Cite

Rupshikha, D., Phukon, M., Kusre, G., Satyanarayana, N., & Sunitha, P. (2012). Prune belly syndrome - A case report. Journal of College of Medical Sciences-Nepal, 7(3), 48–52. https://doi.org/10.3126/jcmsn.v7i3.6709

Issue

Vol. 7 No. 3 (2011)

Section

Case Reports

License

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