Kartagener Syndrome: Congenital Variety of Primary Ciliary Dyskinesia with Infertility

Authors

  • Amit Nandan Dhar Dwivedi Subharati Medical College, Swami Vivekanand Subharati University, Meerut, India

DOI:

https://doi.org/10.3126/ajms.v1i1.2605

Keywords:

Immotile cilia syndrome, primary ciliary dyskinesia (PCD), situs inversus, chronic sinusitis, bronchiectasis

Abstract

We report a rare case of Kartagener's Syndrome, congenital variety of Primary Ciliary Dyskinesia (PCD) with infertility. The patient exhibited the classical triad of which was elucidated by Manes Kartagener in 1933. The frequency of KS in the United States is 1 case per 32,000 live births. Situs inversus occurs randomly in half the patients with PCD; therefore, for every patient with KS, another patient has PCD but not situs inversus.  Current nomenclature classifies all congenital ciliary disorders as PCDs in order to differentiate them from acquired types. KS is part of the larger group of disorders referred to as PCDs. Approximately one half of patients with PCD have situs inversus and, thus, are classified as having KS.

Keywords: Immotile cilia syndrome; Primary ciliary dyskinesia (PCD); Situs inversus; Chronic sinusitis; Bronchiectasis.

DOI: 10.3126/ajms.v1i1.2605

Asian Journal of Medical Sciences Vol.1(1) 2010 p.16-17

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Author Biography

Amit Nandan Dhar Dwivedi, Subharati Medical College, Swami Vivekanand Subharati University, Meerut, India


Assistant Professor,
Department of Radiology
Subharati Medical College,
Swami Vivekanand Subharati University, Meerut, India

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Published

2010-05-07

How to Cite

Dwivedi, A. N. D. (2010). Kartagener Syndrome: Congenital Variety of Primary Ciliary Dyskinesia with Infertility. Asian Journal of Medical Sciences, 1(1), 16–17. https://doi.org/10.3126/ajms.v1i1.2605

Issue

Vol. 1 No. 1 (2010)

Section

Original Articles

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