Complete Androgen Insensitivity Syndrome with Sertoli Cell Adenoma: A Case Report and Review of Literature
DOI:
https://doi.org/10.3126/njr.v1i1.6327Keywords:
Complete androgen insensitivity syndrome, Sertoli cell adenoma, Primary amenorrhoeaAbstract
Complete androgen insensitivity syndrome is a rare X-linked recessive disorder. In patients with this syndrome, testicular tumors, especially seminoma, may develop after puberty. Gonadal malignancies like sertoli cell tumor, yolk sac tumor; embryonic teratoma and unclassified sex cord stromal tumor are rare in these patients. We present here, a case of complete androgen insensitivity syndrome with sertoli cell adenoma in a 25 years old patient who presented to us with history of primary amenorrhoea and bilateral inguinal swellings and was managed with bilateral gonadectomy.
DOI: http://dx.doi.org/10.3126/njr.v1i1.6327
Nepalese Journal of Radiology Vol.1(1): 61-64
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